Rabbit Anti-SGSH Polyclonal Antibody
Cat No | BIOS-1103P |
Conjugate | |
Type | 多克隆抗體 |
Source | Rabbit |
Size | 1mg |
Application | WB |
Format | Liquid |
Concentration | Please refer to the vial lable for the specific concentration. |
Buffer | Supplied in 0.01 M PBS; pH 7.4. |
Storage | Store at -20 degree for long term. |
Synonyms | SGSH;HSS;MPS3A;SFMD |
Purification | Affinity purification |
MolecularWeight | 63KDa |
Description | |
Background | This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A; one type of the lysosomal storage disease mucopolysaccaridosis III; which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. |
We can offer labeled proteins/antibodies using a broad range of intensely fluorescent dyes and labels including FITC, Biotin, Alexa Fluor, Rhodamine B, Cy, Co-Au.